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Affected organs and lesions include retinal hemangioblastomas, cerebellar, brainstem and spinal cord hemangioblastomas, endolymphatic sac tumors, renal cell carcinomas, pheochromocytomas, pancreatic cysts, microcystic serous adenomas, neuroendocrine tumors, as well as epididymal cystadenomas [58-61].
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